High Molecular Weight Kininogen Deficiency – Acquired
At a Glance Acquired high molecular weight kininogen (HK) deficiency is extremely rare. Antibody Baltimore is an antibody to factor XI that blocks high molecular weight kininogen binding and factor XIIa activation of factor XI (Blood 72:1748, 1988). It was associated with urinary tract bleeding. This antibody is to factor XI, not HK. Antibodies to…