Xinghua Gao

Are You Confident of the Diagnosis? Erythrokeratodermia variabilis (EKV) also called erthrokeratodermia figurate variabilis, erythrokeratoderma congenitals progressiva symmetrica, erythrokeratoderma progressive, is a rare genodermatosis characterized by variable migratory erythematous and relatively stable keratotic lesions. What you should be alert for in the history The patients initially present with lesions that are most prevalent during childhood…

Are You Confident of the Diagnosis? What you should be alert for in the history The lesions usually appear soon after birth and progress during childhood. After puberty, the lesions may remain stable or regress partially. Characteristic findings on physical examination Progressive symmetric erythokeratoderm (PSEK) is characterized by well-demarcated hyperkeratotic plaques on erythematous bases symmetrically…