Acanthoma [Granuloma] fissuratum mucosae [oral mucosa], Acanthoma [Granuloma] Fissuratum cutis [ear, nose et cetera]
Acne keloidalis, Acne Keloidalis Nuchae (AKN), Keloid Folliculitis, Folliculitis Keloidalis Nuchae, Nuchal Keloid A, Dermatitis Papillaris Capillitii)
Acquired Perforating Dermatosis (Perforating Dermatoses [All variants], Elastosis Perforans Serpiginosa, Reactive Perforating Collagenosis, Kyrle’s Disease, Perforating Folliculitis, Perforating Periumbilical Calcific Elastosis, Perforating Disorder of Renal Disease)
Acrodermatitis enteropathica (Brandt syndrome, Danbolt – Close syndrome, Danbolt syndrome, Danbolt’s syndrome, Hereditary acrodermatitis enterohepatica, Primary zinc malabsorption)
Actinic prurigo (solar dermatitis, solar prurigo, hereditary polymorphic light eruption, familial actinic prurigo)
Aphthous Stomatitis (Canker Sores, Recurrent Aphthous Stomatitis, Simple Aphthosis, Complex Aphthosis)
Becker's nevus (Becker's melanosis, Becker's pigmentary hamartoma, nevoid melanosis, pigmented hairy epidermal nevus)
Bowenoid Papulosis (Penile Intraepithelial Neoplasia, Squamous Intraepithelial Lesion, Squamous Cell Carcinoma In Situ)
Bullous congenital ichthyosiform erythroderma (epidermolytic hyperkeratosis, keratinopathic ichthyosis)
Buschke-Ollendorff syndrome (dermatofibrosis lenticularis disseminata, connective tissue nevus with osteopoikilosis)
Central Centrifugal Cicatricial Alopecia (Hot comb alopecia, Follicular degeneration syndrome, Scarring alopecia of African-American women, Hot oil alopecia, Cosmetic alopecia, Central elliptical pseudopelade)
Chondrodermatitis Nodularis Helicis (Chondrodermatitis, Chondrodermatitis nodularis chronica helicis, Chondrodermatitis nodularis chronica helicis et antihelicis, Ear corn)
Chronic Mucocutaneous Candidiasis (candidiasis of unspecified site), unspecified disorder of immune mechanism)
Chronic actinic dermatitis (persistent light reaction, actinic reticuloid, photosensitivity dermatitis, photosensitive eczema, photosensitivity and actinic reticuloid (PD/AR) syndrome)
Clear cell acanthoma (Pale cell acanthoma, Degos acanthoma, and Acanthome cellules claires of Degos and Civatte)
Congenital Ichthyosiform Erythroderma (Nonbullous Congenital Ichthyosiform Erythroderma, Autosomal Recessive Congenital Ichthyosis)
Conradi-Hünermann syndrome (CDPX2, chondrodysplasia punctata 2; chondrodysplasia punctata, X-linked dominant form; Conradi-Hünermann-Happle syndrome, Happle syndrome)
Contact Urticaria Syndrome (Contact Urticaria, Nonimmunologic Contact Urticaria, Immunologic Contact Urticaria, Protein Contact Dermatitis)
Corn/callus (singular: callus, callosity, tyloma; plural: callosities, tylomas, tylomata) Clavus (clavi; singular: clavus, corn, heloma; plural: corns, helomas, helomata)
Cowden Syndrome (PTEN Hamartoma Tumor Syndrome, Multiple Hamartoma Syndrome, Bannayan-Riley-Ruvalcaba Syndrome, Lhermitte-Duclos Syndrome)
Cryofibrinogenemia (cold-related gelling or agglutination, Cutaneous manifestations of microvascular occlusion syndromes
Cryoglobulinemia (Cold-related gelling, Cold- related agglutination, Cutaneous manifestations of microvascular occlusion syndromes, Cryoglobulinemic syndrome [clinically asymptomatic]), Cryoglobulinemic vasculitis (clinically apparent disease process)
Cryopyrin Associated Periodic Syndrome (Familial Cold Urticaria, Familial Cold Autoinflammatory Syndrome, Muckle Wells Syndrome, Neonatal Onset Multisystem Inflammatory Disorder, Chronic Infantile Neurologic Cutaneous and Articular Syndrome)
Cutaneous Endometriosis (umbilical endometriosis,cicatricial endometriosis, endometrioma, or ectopic endometrial tissue)
Cutaneous Reactive Angiomatoses (Angioendotheliomatosis, Diffuse Dermal Angiomatosis, Acroangiodermatitis)
Cutaneous lupus mucinosis (Papulonodular mucinosis, papular and nodular mucinosis of lupus, papular and nodular mucinosis of Gold)
Cutaneous lymphoid hyperplasia (lymphocytoma cutis, lymphadenosis benigna cutis, cutaneous lymphoplasia, pseudolymphoma of Spiegler-Fendt)
Dabska tumor (Dabska-type Hemangioendothelioma Endovascular Papillary Angioendothelioma, Hobnail Hemangioendothelioma, Malignant Endovascular Papillary Angioendothelioma, Papillary Intralymphatic Angioendothelioma)
Degos Disease (Kohlmeier Disease, Degos-Kohlmeier Disease, Malignant atrophic papulosis, benign atrophic papulosis, Malignant atrophic papulosis)
Demodicidosis (Other acariasis, including chiggers and Demodex folliculorum or Trombicula infestation)
Dissecting cellulitis of the scalp (perifolliculitis abscedens et suffodiens, Hoffman disease, dissecting folliculitis, follicular occlusion triad)
Dystrophia Unguium Mediana Canaliformis (Canaliform dystrophy of the nails, Canal-like median dystrophy, Dystrophia mediana canaliformis, Dystrophia unguium mediana canaliformis of Heller, Lateral canal-like dystrophy, longitudinal single nail groove, Median canaliform dystrophy, median canaliform nail dystrophy, median canal-like dystrophy of the nail, median nail dystrophy, naevus striatus symmetricus of the thumbs.
Ecthyma gangrenosum (dermatitis gangrenosa infantum, disseminated cutaneous gangrene, pemphigus gangrenosus, rupia escharotica; Septicemia due to Pseudomonas)
Encephalocele (Cephalocele; Encephalocystocele; Encephalomyelocele; Hydroencephalocele; Hydromeningocele, cranial; Meningocele; Meningoencephalocele)
Enteroviral exanthems (Hand, foot, and mouth disease / vesicular stomatitis and exanthem; Herpangina / vesicular pharyngitis; Viral exanthem unspecified)
Epidermal Nevus, including Inflammatory Linear Verrucous Epidermal Nevus (Nevus Verrucosus, Dermatitic Epidermal Nevus)
Erosive Pustular Dermatitis Of The Scalp (Erosive pustulosis of the scalp, Erosive pustular dermatosis of the scalp, Pustular dermatitis of the scalp)
Erythrokeratodermia variabilis (erythrokeratodermia figurate Variabilis, erythrokeratoderma congenitals progressiva symmetrica, erythrokeratoderma progressive)
Erythropoietic Protoporphyria (Protoporphyria, Heme synthetase deficiency, Ferrochelatase deficiency, X-linked dominant protoporphyria [XLDPP], Erythrohepatic protoporphyria [no longer used])
Extranodal NK/T cell lymphoma nasal-type (lethal midline granuloma, polymorphic reticulosis, ENKL, NTCL, midline malignant reticulosis)
Eyelid Dermatitis (xeroderma of the eyelids, eczema of the eyelids, atopic dermatitis, allergic contact dermatitis, irritant contact dermatitis, seborrheic dermatitis of the eyelids)
Fabry Disease (Anderson-Fabry Disease, Alpha-Galactosidase A Deficiency, Angiokeratoma Corporis Diffusum, Ceramide Trihexosidase Deficiency, Fabry's Disease, GLA Deficiency, Hereditary Dystopic Lipidosis)
Familial Cutaneous Leiomyomatosis (FCL) (Hereditary Multiple Leiomyomas, Hereditary Leiomyomatosis and Renal Cell Cancer [HLRCC], Multiple Cutaneous and Uterine Leiomyomatosis, Reed Syndrome)
Favre-Racouchot Syndrome (Nodular Elastosis [Elastoidosis] with Cysts and Comedones, Senile or Solar Comedones, Smokers' Comedones)
Green Nail Syndrome (GNS, Pseudomonas nail infection, chloronychia, green striped nails, chromonychia)
Grover’s Disease (transient acantholytic dermatosis [TAD], persistent acantholytic dermatosis, transient acantholytic dyskeratosis)
Gyrate erythema (superficial or deep) (figurate erythema, annular erythema, reactive erythema, annular erythema, erythema perstans, erythema gyratum perstans, erythema gyratum repens, Darier erythema, erythema figuratum perstans, erythema annulare centrifigum [EAC], Erythema marginatum rheumaticum [EMR], Annular erythema of childhood)
Heavy Metal Dermatoses: Mercury(Mercury dermatosis: Hydrargyria, mercurialism, acrodynia, "pink disease," Mad Hatter’s disease, Hatter’s disease, Minamata disease)
Hemangiomas (infantile hemangiomas, common hemangiomas, strawberry hemangiomas, capillary hemangiomas)
Henoch-Schönlein purpura (Anaphylactoid purpura, Cutaneous small vessel vasculitis secondary to circulating IgA immune complexes, Purpura rheumatica, Schönlein-Henoch Purpura)
Homocystinuria (Homocystinuria due to cystathionine beta-synthase deficiency, classic homocystinuria, cystathionine beta-synthase deficiency)
Ichthyosis, X-linked (Steroid sulfatase deficiency; STS deficiency; Placental steroid sulfatase deficiency; Steroid sulfatase deficiency disease)
Incontinentia Pigmenti (Bloch-Siemens syndrome, Bloch-Sulzberger syndrome, Bloch-Sulzberger disease, melanoblastosis cutis, naevus pigmentosus systematicus)
Infantile Digital Fibromatosis (Reye tumor, recurring digital fibrous tumor of childhood, fibrous tumor of infancy, infantile dermal fibromatosis, juvenile dermatofibroma, subdermal fibromatous tumor of infancy, inclusion body fibromatosis)
Infantile Perianal Pyramidal Protrusions (Infantile Perineal Protrusion. Infantile Perianal Protrusion)
Intravascular Papillary Endothelial Hyperplasia (Angiomatosis, intravascular endothelial proliferation, Masson’s intravascular hemangioendothelioma, Intravenous atypical vascular proliferation, Intravascular angiomatosis, Intravascular endothelial proliferation, Masson’s pseudoangiosarcoma, Masson’s lesion, Masson’s tumor, Hémangioendothéliome Végétante Intravasculaire, Endovasculite proliférante Thrombopoïétique
Juvenile Plantar Dermatosis (atopic winter feet, forefoot dermatosis, sweaty sock dermatitis, peridigital dermatosis, dermatitis plantaris sicca, moon-boot foot syndrome)
Keratin Granuloma (inflamed or ruptured cyst, inflamed or ruptured epidermal inclusion cyst, inflamed or ruptured epidermoid cyst, inflamed or ruptured sebaceous cyst)
Keratolysis exfoliativa (Lamellar dyshidrosis, Recurrent focal palmar peeling, Recurrent palmar peeling)
Keratosis Lichenoides Chronica (Nekam disease, lichen ruber moniliformis, lichen ruber acuminatus, lichen ruber planus, porokeratosis striata lichenoides, lichen verucosus et reticularis, lichenoid tri-keratosis)
Kimura's Disease (Kimura Disease, subcutaneous eosinophilic lymphoid granuloma, inflammatory angiomatous nodule, atypical pyogenic granuloma, eosinophilic hyperplastic lymphogranuloma, eosinophilic granuloma of lymph node and soft tissue, eosinophilic lymphfolliculoid granuloma of soft tissue, eosinophilic lymphofolliculosis)
Kindler Syndrome (Poikiloderma, hereditary acrokeratotic; Bullous acrokeratotic poikiloderma of Kindler and Weary; Poikiloderma, congenital with bullae Weary type)
Klippel-Trenaunay Syndrome (vascular malformation-deregulated growth syndrome[s], VM-DG type 3/Girth type/Klippel-Trenaunay type, KTS, Klipppel-Trenaunay-Weber, and angioosteohypertrophy syndrome
Knuckle Pads (Heloderma, Athlete's Nodules, Surfer's Nodules, Running/Nike Nodules, Subcutaneous Fibroma, Keratosis Supracapitularis, Discrete Keratoderma, Tylositas Articuli)
LEOPARD Syndrome (Lentigines, EKG abnormalities, Ocular Hypertelorism, Pulmonary stenosis, Abnormal Genitalia, Retarded Growth, Deafness; Also known as Multiple lentigines syndrome and Cardiocutaneous syndrome, Gorlin syndrome II, Cardio-Cutaneous syndrome, Lentiginosis profusa, Moynahan syndrome, or Progressive Cardiomyopathic Lentiginosis)
Langerhans Cell Histiocytosis (all variants: Hashimoto-Pritzker disease, congenital self-healing reticulohistiocytosis, Hand-Schöller-Christian disease, Letterer-Siwe syndrome, eosinophilic granuloma)
Leukemia Cutis (Leukemia specific skin lesions, myelosarcoma, granulocytic sarcoma, monoblastic sarcoma, chloroma, primary extramedullary leukemia, aleukemic leukemia cutis)
Lichen Sclerosus et Atrophicus (lichen sclerosus [preferred term], lichen planus atrophicus, lichen planus sclerosus, kraurosis vulva, balanitis xerotica obliterans, vulvar dystrophy)
Linear IgA Dermatosis and Chronic Bullous Dermatosis of Childhood (Linear IgA Disease, linear IgA bullous dermatosis [LABD], Chronic Bullous Dermatosis of Childhood)
Lipoid Proteinosis (Urbach-Wiethe disease, hyalinosis cutis et mucosae, lipoid proteinosis cutis et mucosae, lipoglycoproteinosis)
Lobomycosis (Lacazia loboi, Lobo's disease, Jorge Lobo's disease, keloidal blastomycosis, lacaziosis, leprosy of the Caiabi's)
Loose Anagen Syndrome (pluckable hair, loose hair syndrome, loose anagen hair syndrome, syndrome of loosely attached hair in childhood)
Lupus (profundus) Panniculitis (Lupus Erythematosus Panniculitis, Lupus Panniculitis, Subcutaneous Lupus Erythematosus, Lupus Profundus)
Median Rhomboid Glossitis (posterior midline atrophic candidiasis, central papillary atrophy of the tongue, posterior lingual papillary atrophy)
Melanocytic Nevi, Including Atypical Nevi (Dysplastic Nevi, Nevus with Architectural disorder and Cytologic Atypia)
Meningiococcemia (Menningococcemia (Menningiococcemia, Meningococcal bacteremia, Meningococcal septicemia)
Meningocele, cerebral (Encephalocele; Cephalocele; Encephalocystocele; Encephalomyelocele; Hydroencephalocele; Hydromeningocele, cranial; Meningoencephalocele)
Menkes’ Syndrome (Menkes disease, copper transport disease, steely hair disease, kinky hair disease, or Menkes kinky hair syndrome)
Michelin Tire Baby Syndrome (congenital multiple circumferential skin folds, multiple benign ring-shaped creases of the skin]
Microcystic Adnexal Carcinoma (syringomatous carcinoma, malignant syringoma, group 1 sclerosing sweat gland carcinoma, syringomatous adenoma of the nipple)
Mondor’s disease (Mondors disease, Superficial thrombophlebitis of the veins of the anterolateral thoracoabdominal wall)
Morsicatio Buccarum (morsicatio buccarum et labiorum, cheek biting, repetitive cheek biting, habitual cheek biting, chronic cheek biting, chronic cheek chewing)
Mucous Cysts (mucoid cyst, mucinous pseudocyst, myxomatous cutaneous cyst, synovial cyst, periungual ganglion, nail cyst, digital myxoid cyst, cutaneous myxoid cyst
Mucous Membrane Pemphigoid (mucous membrane [cicatricial] Pemphigoid, cicatricial pemphigoid, anti-epiligrin cicatricial pemphigoid, benign mucous membrane pemphigoid, benign mucosal pemphigoid)
Nail-Patella Syndrome (Hereditary osteo-onychodysplasia (HOOD), Fong disease, Turner-Kieser syndrome, Osterreicher-Turner Syndrome)
Necrotic Drug eruptions (Heparin-induced skin necrosis; warfarin-induced skin necrosis (Coumadin® necrosis)
Necrotizing Fasciitis (Synergistic Necrotizing Cellulitis, Fournier’s Gangrene, Hemolytic Streptococcal gangrene, Meleney’s ulcer, suppurative fasciitis, Ludwig’s angina)
Neonatal cephalic pustulosis (transient cephalic neonatal pustulosis, benign cephalic pustulosis, cephalic pustulosis)
Nephrogenic Systemic Fibrosis (nephrogenic fibrosing dermopathy, scleromyxedema-like illness of renal disease)
Neurofibromatosis (von Recklinghausen disease, central neurofibromatosis, schwannomatosis [neurilemmomatosis])
Neutrophilic Eccrine Hidradenitis (Palmoplantar Eccrine Hidradenitis, (Infectious Eccrine Hidradentitis)
Palisaded Encapsulated Neuroma (Neuroma [PEN and traumatic], Solitary Circumscribed Neuroma, and Traumatic Neuroma (Amputation Neuroma)
Papillon-Lefévre Syndrome (Papillon Lefevre Disease, Juvenile Periodontosis with Hyperkeratosis, Keratosis PalmoPlantaris with Periodontopathia,Palmoplantar keratoderma with periodontosis,Hyperkeratosis palmoplantaris with Periodontosis, PLS Syndrome,palmar plantar hyperkeratosis with concominant periodontal destruction,Palmar-Plantar Hyperkeratosis Periodontal Destruction,PLS Cochin Jewish Disease,Synonym/Haim-Munk Syndrome)
Pemphigus Vegetans (Pemphigus vegetans of Hallopeau, pemphigus vegetans of Neumann, pemphigus vulgaris)
Perianal Streptococcal Disease (perianal streptococcal cellulitis or dermatitis, perineal streptococcal dermatitis, perianal bacterial dermatitis)
Phytophotodermatitis (Irritant photocontact dermatitis due to plants, Phototoxic contact dermatitis due to plants)
Pigmented Purpuric Eruptions (all variants: Schamberg’s disease [capillaritis], Purpura annularis telangiectodes of Majocchi, Pigmented purpuric lichenoid dermatitis of Gougerot and Blum, Lichen aureus, Eczematid-like purpura of Doucas and Kapetanakis)
Pitted Keratolysis (keratolysis plantare sulcatum, keratolysis sulcata, plantar keratolysis sulcatum, keratolysis punctata, sulcate plantare keratolysis)
Pityriasis Lichenoides et Varioliformis Acuta (Mucha Habermann, Mucha-Haberman Disease, Acute Febrile Mucha-Haberman Disease)
Polycystic Ovarian Syndrome (Stein-Leventhal syndrome, polycystic ovarian disease, functional ovarian hyperandrogenism, ovarian hyperthecosis, sclerocystic ovary syndrome)
Polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes (POEMS) syndrome(osteosclerotic myeloma, Crowe-Fukase syndrome, Takatsuki syndrome, Plasma cell dyscrasia, endocrinopathy, polneuropathy [PEP])
Post-inflammatory Hyperpigmentation and Hypopigmentation (post-inflammatory hypermelanosis, post-inflammatory hypomelanosis)
Progressive Symmetric Erythrokeratoderma (Progressive symmetric erythrokeratodermia, Symmetrical progressive erythrokeratodermia, Erythrokeratodermia figurata variabilis, Gottron’s syndrome, Darier-Gottron syndrome)
Pruritic Urticarial Papules and Plaques of Pregnancy (polymorphic eruption of pregnancy, toxemic erythema of pregnancy, and late prurigo of pregnancy)
Pseudocyst of the Auricle (cystic chondromalacia, endochondral pseudocyst, benign idiopathic cystic chondromalacia)
Pseudoporphyia (Pseudoporphyria Cutanea Tarda, Drug-Induced Pseudoporphyria, Drug-Induced Pseudoporphyria Cutanea Tarda)
Psychogenic Purpura (Gardner-Diamond syndrome, autoerythrocyte sensitization syndrome, painful bruising syndrome)
p63 Disorders (ankyloblepharon-ectodermal defects-clefting syndrome, ectrodactyly-ectodermal dysplasia-cleft lip/palate syndrome, split hand/foot malformation, acro-dermato-ungual-lacrimal-tooth [ADULT] syndrome, limb-mammary syndrome, Rapp-Hodgkin syndrome, nonsyndromic orafacial clefting, Hay-Wells syndrome)
paracoccidioidomycosis(South American Blastomycosis, Brazilian Blastomycosis, Lutz-Splendore-Almeida disease, Mucocutaneous-lymphangitic paracoccidioidomycosis)
Radiation Dermatitis (radiodermatitis, radiation epidermitis, radiation skin toxicity, acute radiation skin reaction, late radiation skin reaction, post-irradiation morphea)
Reticular Erythematous Mucinosis (REM, REM syndrome, plaque-like cutaneous mucinosis, round-cell erythematosis)
Rubinstein – Taybi Syndrome (Rubinstein syndrome, broad thumb-hallux syndrome, broad thumbs and great toes, characteristic facies and mental retardation)
Scleromyxedema (generalized and sclerodermoid lichen myxedematosus, papular mucinosis, Arndt-Gottron scleromyxedema)
Smallpox (variola, variola major, variola minor, variola vera, alastrim, the pox, variole, viruela, pocken, blattern
Subcutaneous panniculitic T cell lymphoma (subcutaneous ’panniculitis-like’ T-cell lymphoma, previously termed cytophagic histiocytic panniculitis)
Syphilis (primary syphilis, latent syphilis, cardiovascular syphilis, secondary syphilis, tertiary syphilis, neurosyphilis)
Systemic Amyloidosis with Cutaneous Manifestations (Amyloidosis, Primary Systemic Amyloidosis, AL Amyloidosis)
Systemic Contact Dermatitis (Contact Dermatitis, Systemic; Baboon syndrome; Fisher's systemic contact dermatitis; Systemic contact-type dermatitis; Hematogenous contact eczema; Symmetrical Drug-Related Intertriginous and Flexural Exanthem [SDRIFE] Systemic reactivation of allergic contact dermatitis [RCD])
Talon noire (Black heel, calcaneal petechiae, runner’s heel, basketball heel, tennis heel, hyperkeratosis hemorrhagica, pseudochromhidrosis plantaris, chromidrose plantaire, eccrine intracornee, post-traumatic punctuate hemorrhage of the skin, post-traumatic cutaneous intracorneal blood, disseminated punctuate intraepidermal hemorrhage, black palm, playstation thumb, tennis toe)
Tinea Nigra (tinea nigra palmaris, tinea nigra plantaris, pityriasis nigra, keratomycosis nigricans palmaris)
Trichomycosis Axillaris (trichomycosis palmellina, trichobacteriosis palmellina, trichomycosis nodosa, trichobacteriosis axillaris, Paxton’s disease)
Trichothiodystrophy (Tay syndrome, BIDS syndrome, IBIDS syndrome, PIBIDS syndrome,trichothiodystrophy with congenital ichthyosis)
Verrucous carcinoma (papillomatosis cutis, carcinoides of Gottron, epithelioma cuniculatum, Buschke-Lowenstein tumor, Ackerman tumor, oral florid papillomatosis)
vaccinia, progressive and/or smallpox, vaccine(vaccinia necrosum, vaccinia gangrenosa, prolonged vaccinia)
Wiskott-Aldrich Syndrome (Wiskott-Aldrich-Huntley syndrome, eczema-thrombocytopenia-immunodeficiency syndrome)
Xanthoma, eruptive (hyperchylomicronemia, Fredrickson type I hyperlipoproteinemia, Fredrickson type V hyperlipoproteinemia)
Xanthomas, plane (planar xanthoma, palmar xanthoma, intertriginous xanthoma, diffuse xanthoma, xanthelasma)